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4-Methylumbelliferyl 6-Sulfo-2-acetamido-2-deoxy-β-D-glucopyranoside Potassium Salt _分子结构_CAS_210357-38-3)
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4-Methylumbelliferyl 6-Sulfo-2-acetamido-2-deoxy-β-D-glucopyranoside Potassium Salt

产品号 M335000 公司名称 Toronto Research Chemicals
CAS号 210357-38-3 公司网站 http://www.trc-canada.com
分子式 C18H20KNO11S 电 话 +1 (416) 665-9696
分子量 497.5148 传 真 +1 (416) 665-4439
纯 度 电子邮件 info@trc-canada.com
保 存 Hygroscopic, -20°C Freezer, Under Inert Atmosphere Chembase数据库ID: 174532

产品价格信息

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产品别名

标题
4-Methylumbelliferyl 6-Sulfo-2-acetamido-2-deoxy-β-D-glucopyranoside Potassium Salt
IUPAC标准名
potassium [(2R,3S,4R,5R,6S)-5-acetamido-3,4-dihydroxy-6-[(4-methyl-2-oxo-2H-chromen-7-yl)oxy]oxan-2-yl]methyl sulfate
IUPAC传统名
potassium [(2R,3S,4R,5R,6S)-5-acetamido-3,4-dihydroxy-6-[(4-methyl-2-oxochromen-7-yl)oxy]oxan-2-yl]methyl sulfate
别名
7-[[2-(Acetylamino)-2-deoxy-6-O-sulfo-β-D-glucopyranosyl]oxy]-4-methyl-2H-1-benzopyran-2-one Monopotassium Salt
MUGS

产品登记号

CAS号 210357-38-3

产品性质

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外观 White Solid
熔点 190-193°C (dec.)
溶解度 Water
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保存条件 Hygroscopic, -20°C Freezer, Under Inert Atmosphere
保存注意事项 Light Sensitive - Protect from Light; Store at -20°C

产品详细信息

详细说明 (English)
A fluorogenic substrate used for the diagnosis of GM2 gangliosidoses in leukocytes. Genetic defects in human b-hexosaminidase isozymes (Hex A & Hex B) result in various clinical and biochemical types of GM2 gangliosidosis. They include Tay Sachs disease,

参考文献

  • Clinical Genetics, 26, 318 (1984)
  • Bayleran, J., et al.: Clin. Chem. Acta 143, 73 (1984)