4-Methylumbelliferyl α-L-Idopyranosiduronic Acid 2-Sulfate Disodium Salt

• 产品号: M334715
• 分子式: C16H14Na2O12S
• 分子量: 476.3197
• 保 存: Hygroscopic, -20°C Freezer, Under Inert Atmosphere

产品别名

• 标题: 4-Methylumbelliferyl α-L-Idopyranosiduronic Acid 2-Sulfate Disodium Salt
• IUPAC标准名: disodium (2R,3S,4S,5R,6S)-3,4-dihydroxy-6-[(4-methyl-2-oxo-2H-chromen-7-yl)oxy]-5-(sulfonatooxy)oxane-2-carboxylate
• IUPAC传统名: disodium (2R,3S,4S,5R,6S)-3,4-dihydroxy-6-[(4-methyl-2-oxochromen-7-yl)oxy]-5-(sulfonatooxy)oxane-2-carboxylate
• 别名: 4-Methyl-2-oxo-2H-1-benzopyran-7-yl α-L-Idopyranosiduronic Acid 2-(Hydrogen Sulfate); 4-Methylumbelliferyl α-L-Iduronic Acid-2-sulfate Sodium Salt

产品性质

• 外观: White Solid
• 熔点: >220°C (dec.)
• 溶解度: Ethanol
• 溶解度: Methanol
• 溶解度: Water
• 保存条件: Hygroscopic, -20°C Freezer, Under Inert Atmosphere

产品详细信息

详细说明 (English)

A fluorogenic substrate in the assay of α-L-Iduronidase. A fluorimetric enzyme assay for the diagnosis of MPS II (Hunter disease).

参考文献

• Matalon, R., et al.: Biochem. Biophys. Res. Commun., 47, 959 (1972)
• Voznyi, Y.V., et al.: J. Inherit. Metab. Dis., 24, 675 (2001)