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L-α-Hydroxyglutaric acid disodium salt

产品号 90790 公司名称 Sigma Aldrich
CAS号 63512-50-5 公司网站 http://www.sigmaaldrich.com
分子式 C5H6Na2O5 电 话 1-800-521-8956
分子量 192.07768 传 真
纯 度 ≥98.0% (GC) 电子邮件
保 存 Chembase数据库ID: 154925

产品价格信息

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产品别名

标题
L-α-Hydroxyglutaric acid disodium salt
IUPAC标准名
disodium (2S)-2-hydroxypentanedioate
IUPAC传统名
disodium L-2-hydroxyglutarate
别名
Disodium (S)-2-hydroxyglutarate
(S)-2-Hydroxypentanedioic acid disodium salt

产品登记号

Beilstein号 5318042
CAS号 63512-50-5

产品性质

杂质 ≤6.0% water
线性分子式 C5H6O5Na2
纯度 ≥98.0% (GC)
比旋光度 [α]/D -8.5±1.5°, c = 1 in 0.1 M NaOH
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保存温度 2-8°C

产品详细信息

详细说明 (English)
Biochem/physiol Actions
L-alpha-Hydroxyglutaric acid accumulates as a result of a rare defect in L-2-HG dehydogenase, leading to the metabolic disorder L-2-hydroxyglutaric aciduria (L-2HGA). L-2HGA is associated with neuronal defects, leukodystrophy and linked to an increased risk of brain tumors.
详细说明 (简体中文)
Biochem/physiol Actions
L-alpha-Hydroxyglutaric acid accumulates as a result of a rare defect in L-2-HG dehydogenase, leading to the metabolic disorder L-2-hydroxyglutaric aciduria (L-2HGA). L-2HGA is associated with neuronal defects, leukodystrophy and linked to an increased risk of brain tumors.

参考文献